In a small Brazilian town, there resides an extraordinary duo of identical twins named Elis and Eloá. Their story serves as a beacon of resilience and the remarkable power of the human spirit. Afflicted with Hutchinson-Gilford Progeria Syndrome, a rare and fatal genetic disorder causing accelerated aging, these twins confront their adversities with remarkable grace and strength, earning admiration from people worldwide.
Understanding Hutchinson-Gilford Progeria syndrome
HGPS stands as an exceptionally rare disorder, impacting roughly 1 in 20 million newborns globally. Marked by rapid aging from early childhood, individuals with progeria often display growth delays, diminished body fat and hair, prematurely aged skin, joint stiffness, and severe cardiovascular issues. Typically, those with HGPS have an average life expectancy of about 14.5 years, though some may extend into their late teens or early twenties. This syndrome gained public attention through the film The Curious Case of Benjamin Button.
The condition is caused by a mutation in the LMNA gene, which produces the lamin A protein responsible for maintaining the structural integrity of the cell nucleus. The mutation results in the production of an abnormal version of the protein, called progerin, which causes cells to become unstable and die prematurely.
Elis and Eloá’s journey
Elis and Eloá swiftly captured attention because of their distinctive medical condition. Despite the physical hurdles imposed by progeria, their contagious smiles and steadfast optimism have emerged as beacons of hope and inspiration. Guilherme and Elismar, the twins’ parents, have dedicated their lives to offering the utmost care for their daughters, striving to ensure they experience as normal a life as feasible within the confines of their condition.
The family’s path has been far from easy. Their daily life is filled with demanding medical routines, including physiotherapy, aimed at addressing joint stiffness and preserving mobility. Despite these challenges, Elis and Eloá approach each day with remarkable bravery and an unparalleled enthusiasm for life, which is truly remarkable.
A global community of support
Elis and Eloá’s narrative has touched hearts worldwide, sparking a surge of solidarity from individuals and groups committed to promoting awareness about progeria and backing research endeavors. The Progeria Research Foundation, a pivotal entity in this realm, has played a vital role in propelling research forward and furnishing assistance to families grappling with the condition.
Through social media platforms, the twins’ journey is shared with a broad audience, fostering a sense of community and solidarity. Their family’s updates, documenting both the highs and lows of their daily lives, provide invaluable insights into the realities of living with progeria, while also spreading a message of hope and perseverance.
Advances in research and hope for the future
In recent years, there have been remarkable advancements in comprehending and addressing progeria. A notable milestone occurred in 2020 when the U.S. Food and Drug Administration (FDA) granted approval for the first progeria treatment: lonafarnib. This medication has demonstrated efficacy in prolonging the lives of children with progeria by mitigating the accumulation of progerin in cells, thereby decelerating the disease’s advancement.
Though a cure remains elusive, ongoing research presents promising prospects. Scientists are delving into gene-editing methodologies, like CRISPR, as potential means to rectify the genetic mutation at its root. For families such as Elis and Eloá’s, these breakthroughs offer a ray of hope for the future.
And in our other article, we recounted the remarkable story of a girl born without a nose, affectionately dubbed “Voldemort,” who refuses to let her differences define her.
Flight Attendant Reveals Surprising Reason Why Cabin Crew Sits On Their Hands During Take Off and Landing
In the world of air travel, flight attendants do much more than serve drinks and snacks—they are highly trained safety professionals, responsible for the well-being of all passengers. Among the many safety protocols they follow, one unusual practice often catches the eye: flight attendants sitting on their hands during takeoff and landing. While it may look odd to the average traveler, there is an important reason behind this procedure.
Image Credit: @_hennylim_ TikTok
Let’s explore the purpose of this practice and how it plays a critical role in ensuring safety during flights.
The Bracing Position Explained by a Flight Attendant
If you’ve ever noticed flight attendants buckling up in their jump seats and adopting a particular posture—sitting on their hands as the plane takes off or prepares to land—you might wonder what they’re doing. In a viral TikTok video, Cebu Pacific flight attendant Henny Lim sheds light on this often-overlooked protocol.
According to Lim, the posture flight attendants take, known as the bracing position, involves several key actions:
Fastening seatbelts securely
Sitting upright
Placing hands on their thighs with thumbs tucked in
Keeping arms relaxed
Ensuring their feet are flat on the floor
While this position may seem strange to passengers, it’s designed to serve a crucial purpose, especially in the event of an emergency.
Purpose of the Bracing Position
The main goal of the bracing position is to minimize movement and reduce the risk of injury if a crash or emergency landing occurs. During an impact, bodies can be thrown forward with significant force, leading to dangerous, uncontrolled movements, or flailing, which increases the risk of injury. By sitting on their hands and securing themselves, flight attendants limit their body’s motion and protect their limbs from potential harm.
Additionally, flight attendants use this time to mentally prepare for emergency scenarios. As Lim explains, this involves conducting a “silent review” where they mentally go over safety procedures, emergency exits, equipment, and commands. This mental preparation ensures they can act swiftly and effectively in the event of an emergency, prioritizing passenger safety at all times.
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